From: LCAT deficiency: a systematic review with the clinical and genetic description of Mexican kindred
 | Total n = 216 (Unclassified n = 20) | FLD (n = 153, 70.8 %) | FED (n = 43, 19.9 %)) | p | |
---|---|---|---|---|---|
AGE (years) a | 44.8 (±15.6) | 40.2 (±13.8) | 53.0 (±15.6) | <0.001 | |
GENDER ( n  = 203) (Unknown = 13) | MALE | 119 (58.6 %) | 93 (60.7 %) | 18 (41.8 %) | 0.17 |
FEMALE | 84 (41.3 %) | 57 (37.2 %) | 23 (53.4 %) | ||
PREMATURE CHD ( n  = 148) (Unknown = 68) | YES | 13 (6.01 %) | 1 (0.65 %) | 12 (27.9 %) | <0.001 |
NO | 135 (62.5 %) | 112 (73.2 %) | 16 (37.2 %) | ||
HDL-C mg/dL b | 7 (4–12) | 7.0 (4–12) | 6.7 (3.9–9.7) | 0.272 | |
Triglycerides mg/dL b | 206 (138–380) | 185 (121–380) | 283 (164–528) | 0.165 | |
LCAT ACTIVITY nmol/mL/h b ( n  = 78) | 1.50 (0.00-7.02) | 0.1 (0.0–2.1) | 2.1 (0.9–3.5) | 0.013 | |
eGFR < 60 ( n  = 184) (Unknown = 32) | YES | 65 (35.3 %) | 62 (40.5 %) | 3 (6.9 %) | 0.00 |
NO | 87 (47.2 %) | 48 (31.3 %) | 38 (88.3 %) | ||
PROTEINURIA/ MICROALBUMINURIA ( n  = 177) (Unknown = 29) | YES | 84 (47.4 %) | 83 (54.2 %) | 1 (2.32 %) | 0.00 |
NO | 64 (36.1 %) | 24 (15.6 %) | 40 (93.02 %) | ||
HEMOLYTIC ANEMIA ( n  = 215) (Unknown = 30) | YES | 116 (53.9 %) | 115 (75.1 %) | 1 (2.32 %) | 0.00 |
NO | 69 (32.1 %) | 28 (18.3 %) | 20 (46.5 %) |