Skip to main content

Table 3 Comparison between the STSL group and FH group

From: Clinical characteristics of sitosterolemic children with xanthomas as the first manifestation

Indicators

STSL Group

FH Group

P values

Male, n (%)

5 (50%)

4 (40%)

1.00

Age at diagnosis(years), mean ± SD

6.90 ± 4.12

7.01 ± 4.24

0.951

The interval between onset and diagnosis

(years), median (IQR)

1.50 (0.96 ~ 2.56)

1.00 (0.73 ~ 3.75)

0.675

SDS of height, mean ± SD

-0.95 ± 1.21

-0.58 ± 0.87

0.440

BMI (kg/m2), mean ± SD

14.84 ± 2.25

15.39 ± 1.70

0.543

Chol (mmol/L), median (IQR)

Reference range: 2.90–5.17 mmol/L

12.57 (9.55 ~ 14.62)

17.45 (16.04 ~ 21.47)

0.002

LDL-c (mmol/L), mean ± SD

Reference range: 2.07–3.36 mmol/L

9.26 ± 2.71

14.58 ± 4.08

0.003

Hb (g/L), mean ± SD

114.50 ± 8.89

128.40 ± 10.46

0.005

Anemia, n (%)

5 (50%)

0 (0%)

0.033

MCV (fl.), median (IQR)

81.34 (69.35 ~ 83.40)

81.25 (74.50 ~ 85.13)

0.762

PLT (×109/L), mean ± SD

280.34 ± 86.13

290.50 ± 52.15

0.753

MPV (fl.), median (IQR)

11.00 (9.79 ~ 12.53)

8.95 (8.88 ~ 12.28)

0.009

Paternal Chol (mmol/L), median (IQR)

Reference range: 2.90–5.17 mmol/L

5.85 (5.20 ~ 7.08)

(n = 8)

8.18 (6.95 ~ 8.40)

(n = 10)

0.008

Paternal LDL-c (mmol/L), median (IQR)

Reference range: 2.07–3.36 mmol/L

3.82 (3.51 ~ 4.76)

(n = 8)

5.64 (4.93 ~ 6.13)

(n = 10)

0.021

Maternal Chol (mmol/L), mean ± SD

Reference range: 2.90–5.17 mmol/L

5.22 ± 0.50

(n = 8)

6.97 ± 1.28

(n = 10)

0.004

Maternal LDL-c (mmol/L), mean ± SD

Reference range: 2.07–3.36 mmol/L

2.99 ± 0.51

(n = 8)

4.79 ± 1.01

(n = 10)

0.001

  1. SDS of height, standard deviation score of height; MCV, mean corpuscular volume; MPV, mean platelet volume